Clear cell adenocarcinoma arising from abdominal wall endometriosis

In: Cirugía y Cirujanos (English Edition) · 2016 · vol. 84(3) , pp. 245–249 · doi:10.1016/j.circen.2016.04.009 · W2398101841
article OA: diamond CC0 ⤵ 11 in-corpus citations

Abstract

Clear cell carcinoma originating in the abdominal wall is a rare event. It is generally associated with endometrial tissue implants left behind after a caesarean section or other gynaecological operations. Its pathophysiology is complex and controversial. The case is presented of a 45 year-old female with history of three caesarean sections, who was seen due to having a tumour mass of 6 months onset in the anterior abdominal wall. Imaging studies confirmed its location, and due to measuring 9 cm × 7 cm it was suspected to be an urachal tumour. A resection with wide margins was performed. The histopathology report was of a clear cell adenocarcinoma originated in ectopic endometrial tissue, with negative margins. This is a very rare case, with few cases reported in the literature. This diagnosis should be included in tumours of the abdominal wall. El carcinoma de células claras originado en la pared abdominal es una entidad rara y generalmente está asociado a implantes iatrogénicos de tejido endometrial, por una incisión quirúrgica durante la operación cesárea u otros procedimientos ginecológicos, su fisiopatología es compleja y controversial. Paciente del sexo femenino de 45 años con antecedente de 3 cesáreas, que acude con masa tumoral en la pared anterior del abdomen de 6 meses de evolución. Los estudios de imagen confirmaron su localización, con dimensiones de 9 por 7 cm que hicieron sospechar en un tumour del uraco; con ese diagnóstico se decidió llevar a resección amplia. El reporte final de patología fue de adenocarcinoma de células claras originado en foco endometriósico, con márgenes quirúrgicos negativos. Esta entidad es excepcionalmente rara, hay pocos casos publicados, su conocimiento es esencial para incluirla en el diagnóstico diferencial de tumores de pared abdominal.

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endometriosis

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