Extrauterine low-grade endometrial stromal sarcoma: report of three cases
Case report
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⤵ 22 in-corpus citations
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Three cases of extrauterine low-grade endometrial stromal sarcoma, found in the ovary, pelvic, and abdominal cavities, presented with specific histological and immunohistochemical features and showed no recurrence after surgery.
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Abstract
Three cases of rare low-grade endometrial stromal sarcoma of the extrauterine tissue are presented. Each one occurred in the ovary, pelvic and abdominal cavities. Two were associated with endometriosis. Histologically, the tumors were characterized by an infiltrative and diffuse proliferation of uniform round or oval cells, abundant small vessels, low mitotic activity, the presence of foam cells and vascular invasion. Immunohistochemically, all tumors expressed vimentin, muscle markers (desmin, muscle-specific actin and alpha-smooth muscle actin) and progesterone receptors. Two tumors were diploid and one was aneuploid by flow cytometry. All patients were well with no evidence of disease 16-39 months after surgery. It is suggested that this neoplasm may arise with or without endometriosis under hormonal influence. This rare variant of Müllerian tumors should not be confused with adenosarcoma and soft tissue tumors, such as smooth muscle tumors and solitary fibrous tumor.
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Cited by (22)
- Extrauterine Low-Grade Endometrial Stromal Sarcoma: A Case Report and Review of the Literature 2026
- Extra-uterine low grade endometrioid stromal sarcoma arising from ovarian endometriosis: a case report and review of the literature 2019
- Fertility-Sparing Surgery for Patients with Endometrioid Stromal Sarcoma of Ovary: A Case Report with a Review of the Literature 2018
- Primary extragenital endometrial stromal sarcoma of the lung: first reported case and review of literature 2017
- Endometrial Stromal Sarcoma Arising from Endometriosis 2017
- An unexpected diagnosis of primary omental endometrial stromal sarcoma in a patient with acute right abdominal pain: A case report and review of literature 2017
- Endometriosis of Extra-Abdominal Soft Tissues: A Tertiary Center Experience 2016
- A Rare Case of Multiple Malignancies arising in Endometriosis: Diffuse Extra-Uterine High-grade Endometrial Stromal Sarcoma and Ovarian Carcinoma 2015
- Ovarian endometriosis as a premalignant condition: epidemiological, histological and molecular evidence 2012
- Extragenital endometrial stromal sarcoma arising in endometriosis 2012
- A case of primary ovarian low-grade endometrial stromal sarcoma 2012
- Sarcoma del estroma endometrial del ovario. Presentación de un caso y revisión del cuadro clínico-patológico 2010
- Endometrial stromal sarcoma presenting as prevesical mass mimicking urachal tumor 2009
- Bilateral Endometrial Stromal Sarcoma Originating from Ovarian Endometriosis: A Case Report 2009
- Endometrial stromal sarcoma of the small bowel 2008
- Endometrial stromal sarcoma associated with extrauterine endometriosis: a case report and literature review 2008
- A case of high-grade endometrial stromal sarcoma arising from endometriosis in the cul-de-sac 2006
- A case of high-grade endometrial stromal sarcoma arising from endometriosis in the cul-de-sac 2006
- Low-grade endometrial stromal sarcoma presenting as vaginal nodule 2004
- Low-grade endometrial stromal sarcoma with glandular differentiation arising in ovarian endometriosis 2004
- Extrauterine low-grade endometrial stromal sarcoma with florid endometrioid glandular differentiation 2001
- Low-grade endometrial stromal sarcoma of the ectocervix after therapy for breast cancer 2000
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