Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus

Divya K Shah, Divya Shah, Shah DK, Laufer MR, Marc R. Laufer
Fertility and sterility · 2011 · vol. 96(1) , pp. e39–e41 · doi:10.1016/j.fertnstert.2011.05.013 · PMID:21605855 · W2080456719
article OA: closed CC0 ⤵ 1 in-corpus citation
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⚙ AI-generated summary by claude@2026-06, 2026-06-07 ⓘ

This case report describes a patient diagnosed with the Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) syndrome, characterized by the presence of a single uterus.

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Abstract

ObjectiveTo describe an unusual case of obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus.DesignCase report.SettingMajor academic medical center.Patient(s)A 12-year-old girl with OHVIRA syndrome.Intervention(s)None.Main outcome measure(s)None.Result(s)A 12-year-old girl presented with presumed OHVIRA syndrome and had surgical correction of the obstructed hemivagina. Two years later she presented with increasing pelvic pain and underwent laparoscopy for presumed endometriosis. A single uterus with a broad flat fundus was found as well as endometriosis.Conclusion(s)OHVIRA syndrome is typically associated with a didelphys uterus with two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a rare congenital anomaly of the female reproductive tract: OHVIRA syndrome with a single uterus. From a fertility standpoint, cases of a single uterus with two cervices are managed differently than two uteri with two cervices. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.

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Condition tags

endometriosis

MeSH descriptors

Abnormalities, Multiple Kidney Uterus Vagina Abnormalities, Multiple Abnormalities, Multiple Child Endometriosis Endometriosis Endometriosis Female Humans Kidney Kidney Uterus Uterus Vagina Vagina

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References (17)

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Source provenance

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