[Intratumoral endometriosis in renal angiomyolipomas associated to medium vessel necrotizing vasculitis in a patient with Wünderlich syndrome. A rare finding]

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Abstract

Spontaneous perirenal hematoma or Wünderlich syndrome is a rare entity that requires urgent attention. The most frequent causes are renal neoplasms, mainly renal angiomyolipoma, and vascular diseases (vasculitis). We present a case of a woman with a history of renal angiomyolipomas associated with tuberous sclerosis complex, who developed Wünderlich's syndrome associated with medial vessel vasculitis as well as an uncommon instance of intratumoral endometriosis.

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Condition tags

endometriosis

MeSH descriptors

Angiomyolipoma Endometriosis Hematoma Kidney Diseases Kidney Neoplasms Vasculitis Adult Angiomyolipoma Endometriosis Female Hematoma Humans Kidney Diseases Kidney Neoplasms Necrosis Syndrome Vasculitis Vasculitis

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europepmc
last seen: 2026-07-04T06:08:07.471253+00:00
pubmed
last seen: 2026-05-13T22:22:41.077124+00:00
unpaywall
last seen: 2026-05-14T19:30:52.867331+00:00
License: public-domain-us · commercial use OK · attribution required
Courtesy of the U.S. National Library of Medicine