Large leiomyoma in a woman with Mayer-Rokitansky-Kuster-Hauser syndrome.

Large leiomyoma in a woman with Mayer-Rokitansky-Kuster-Hauser syndrome DOI: https://doi.org/10.3941/jrcr.v7i3.1267Keywords: MRKH syndrome, mullerian duct anomalies, leiomyoma, cystic degenerationAbstract Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized as aplasia or hypoplasia of uterus and vagina in women with normal development of secondary sex characteristics. It affects 1 in 4000-5000 female births. Women with this syndrome present with primary amenorrhoea. MRKH syndrome may be associated with renal, skeletal, cardiac and auditory anomalies. Women with MRKH syndrome may develop leiomyoma from a rudimentary uterus, though very rare. Initial investigation in women having MRKH syndrome with leiomyoma is ultrasonography (USG). However, CT and MRI are more accurate to evaluate the pelvic anatomy and pathologies.Downloads Published 2013-03-11 Issue Section Obstetric & Gynecologic Radiology License The publisher holds the copyright to the published articles and contents. However, the articles in this journal are open-access articles distributed under the terms of the Creative Commons Attribution-NonCommercial-NoDerivs 4.0 License, which permits reproduction and distribution, provided the original work is properly cited. The publisher and author have the right to use the text, images and other multimedia contents from the submitted work for further usage in affiliated programs. Commercial use and derivative works are not permitted, unless explicitly allowed by the publisher.