Epithelioid sarcoma: the challenge of providing the optimal treatment.

Epithelioid sarcoma are rare malignant mesenchymal tumors that affect mostly young males in the distal part of extremities. They are frequently treated initially with incomplete resection because of their clinically slow-growing benign pattern. Heterogeneity in pathological presentation of epithelioid leads to frequent misdiagnosis that affects survival. This report describes the clinical course and management of a 58-year-old man who presented with epithelioid sarcoma in the shoulder girdle. The case was misdiagnosed initially as a benign lesion and then, at the local recurrence, as a carcinoma. The patient is free of recurrence and metastases 4 years after a large resection of the axillary lymph recurrence sacrificing the axillary vein followed by radiation.