Adult Omental Alveolar Rhabdomyosarcoma: an unusual site. A case report and literature review

Background: Omental alveolar rhabdomyosarcoma in adults is a very hazardous tumor. Its pathogenesis is still under discussion and many studies consider it different from its pediatric counterpart. This tumor can arise from any soft tissue in the body thus it can be found anywhere, but it's found mainly in the head and neck region. Omentum as the primary site was reported only by six studies in the English literature before. In this paper we aim to report the seventh case and perform a review of all paperworks that pertains to this topic. Case Presentation: we present a case of a 52 years old smoker male. His medical record was not significant. He presented with dull pain in the right iliac fossa. He had suffered from generalized abdominal pain in the past several months but this time the pain was unbearable. On examination he had a palpable mass in the region. CT revealed a mass arising from omentum. A laparotomy was performed and biopsies were taken, stained, examined and led to the diagnosis of ARMS. The patient was put on radio and chemo-therapy. He missed some appointments after that. When he was admitted 2 months later he was suffering from neurological symptoms which after performing lumbar puncture turned out to be tumor metastasis. Regrettably the patient died after his second cycle of chemotherapy. Conclusion: Adult rhabdomyosarcomas are rare tumors that can arise from any soft tissue including omentum and should be taken into consideration when we deal with primary tumors originating from that area. The studies and our understanding for this neoplasm is still so limited and should be expanded widely.