A rare case of cervical dysgenesis presented with endometriosis and ectopic kidney

A rare case of cervical dysgenesis presented with endometriosis and ectopic kidney DOI: https://doi.org/10.18203/2320-1770.ijrcog20221310Keywords: Cervical dysgenesis, Endometriosis, HysterectomyAbstract Cervical dysgenesis is a rare cause of obstructive amenorrhoea. We are presenting a case of a 15-year-old girl presented with primary amenorrhoea diagnosed with cervical dysgenesis with left ectopic kidney and endometriosis. The patient underwent laparoscopy followed by exploratory laparotomy with total abdominal hysterectomy with left salpingectomy followed by neovaginal creation and right ureteric D-J stenting and vaginal mould insertion. Cervical agenesis treatment should aim at the re-establishment of patency of the outflow tract. A fistulous tract with stent placement has been done in some cases but eventually, hysterectomy is required in view of recurrent and severe pelvic infection is a common problem. Ovarian function can be preserved if a hysterectomy is performed timely. Metrics References Kiran Z, Jamil T. Primary amenorrhoea secondary to two different syndromes: a case study. BMJ Case Rep. 2019;12(3):e228148. Koyama‐Sato M, Hashida O, Nakamura T, Hirahara F, Sakakibara H. Case of early postoperative adhesion in a patient with molimina due to transverse vaginal septum concomitant with imperforate hymen. J Obstet Gynaecol Res. 2015;41(7):1141-4. Kahn R, Duncan B, Bowes DW. Spontaneous opening of congenital imperforate hymen. J Pediatr. 1975;87:768-70. Rock JA, Jones HW 3rd, Te Linde′s Operative Gynecology. 10th ed. Wolters Kluwer India: Lippincott Williams and Wilkins; South Asian edition. 2008. Creighton SM, Davies MC, Cutner A. Laparoscopic management of cervical agenesis. Fertil Steril. 2006;85:1510.e13-5. Rock JA, Carpenter SE, Wheeless CR, Jones HW. The clinical management of maldevelopment of the uterine cervix. J Pelvic Surg. 1995;1:129-33. The American Fertility Society classifications of adnexal adhesions, distal tubal occlusion, tubal occlusion secondary to tubal ligation, tubal pregnancies, Mullerian anomalies and intrauterine adhesions. Fertil Steril. 1988;49:944-55. Lai TH, Wu MH, Hung KH, Cheng YC, Chang FM. Successful pregnancy by transmyometrial and transtubal embryo transfer after IVF in a patient with congenital cervical atresia who underwent uterovaginal canalization during caesarean section. Hum Reprod. 2001;16:268-71. Grimbizis GF, Tsalikis T, Mikos T, Papadopoulos N, Tarlatzis BC, Bontis JN. Successful end-to-end cervico-cervical anastomosis in a patient with congenital cervical fragmentation: Case report. Hum Reprod. 2004;19:1204-10. Rock JA, Roberts CP, Jones HW Jr. Congenital anomalies of the uterine cervix: Lessons from 30 cases managed clinically by a common protocol. Fertil Steril. 2010;94:1858-63.