Obstructed Mullerian Anomalies and Endometriosis in the Adolescent

In: Endometriosis in Adolescents · 2020 · pp. 273–287 · doi:10.1007/978-3-030-52984-0_12 · W3102802278
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Obstructed Mullerian anomalies in adolescents can cause endometriosis, and early diagnosis and correction are crucial for preventing complications.

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This chapter reviews obstructive Müllerian anomalies in adolescents, focusing on how obstructed outflow can cause retrograde menstruation and thereby contribute to endometriosis. It outlines high-level diagnostic elements (history, physical exam, labs, and imaging) and discusses classification systems as well as presentation and management across common entities such as OHVIRA (obstructed hemivagina ipsilateral renal anomaly) and unicornuate uterus with obstructed uterine horn, plus rarer anomalies like cervical agenesis and uterine isthmus agenesis. A key caveat highlighted is that early diagnosis and timely correction are considered paramount to prevent progression of severity and associated complications, implying that delays can change outcomes. This paper is centrally about endometriosis — it specifically links obstructed Müllerian anomalies and retrograde menstruation to endometriosis development in adolescents.

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Abstract

Obstructive Mullerian anomalies can lead to retrograde menstruation and as such have been shown to cause endometriosis in the adolescent. Appropriate and early diagnosis and timely correction are paramount in preventing progression of severity and avoiding associated complications. Key elements for the diagnosis of obstructive Mullerian anomalies include a careful history, physical exam, laboratory studies, and imaging. Various classification systems have been proposed, which can aid in diagnostic description as well as approach to treatment. The presentation and management of the most well-known anomalies such as obstructed hemivagina ipsilateral renal anomaly syndrome (OHVIRA) and unicornuate uterus with obstructed uterine horn as well as more rare presentations such as cervical agenesis and uterine isthmus agenesis as well as other complex uterine anomalies are discussed. Access this chapter Tax calculation will be finalised at checkout Purchases are for personal use only Similar content being viewed by others

References

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Use of autologous micromucosa graft for vaginoplasty in vaginal agenesis. Ann Plast Surg. 2009;63:645–9. Author information Authors and Affiliations Corresponding author Editor information Editors and Affiliations Rights and permissions Copyright information © 2020 Springer Nature Switzerland AG About this chapter Cite this chapter Petrini, A., Pasternak, M., Pfeifer, S.M. (2020). Obstructed Mullerian Anomalies and Endometriosis in the Adolescent. In: Nezhat, C.H. (eds) Endometriosis in Adolescents. Springer, Cham. https://doi.org/10.1007/978-3-030-52984-0_12 Download citation DOI: https://doi.org/10.1007/978-3-030-52984-0_12 Published: Publisher Name: Springer, Cham Print ISBN: 978-3-030-52983-3 Online ISBN: 978-3-030-52984-0 eBook Packages: MedicineMedicine (R0)

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