Anesthetic Management of a Patient With Bernard-Soulier Syndrome and Catamenial Hemothorax for Thoracotomy: A Case Report

Kaniyil S, Suvarna Kaniyil, Ananya Soman, Soman A, Indu Susheela, Susheela I
A&A practice · 2025 · vol. 19(10) , pp. e02064 · doi:10.1213/XAA.0000000000002064 · PMID:41117791
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⚙ AI-generated deep summary by claude@2026-06, 2026-06-20 · read from full text ⓘ

This case report describes anesthetic management for a 22-year-old woman with Bernard-Soulier syndrome, an inherited platelet bleeding disorder, and catamenial hemothorax, a rare manifestation of thoracic endometriosis with recurrent menstruation-associated intrapleural bleeding, who underwent thoracotomy and pleurodesis. The authors emphasize that the coexistence of these disorders creates compounded perioperative challenges related to hemorrhage risk and respiratory complications, and they present a successful perioperative course. A major limitation is that it is a single-patient case report with only a brief literature review, so findings cannot be generalized. This paper is centrally about endometriosis — specifically thoracic endometriosis presenting as catamenial hemothorax, in the context of anesthesia for thoracotomy.

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Abstract

Bernard-Soulier syndrome is a rare inherited bleeding disorder caused by a deficiency of the platelet surface glycoprotein Ib-IX-V complex, leading to defective platelet adhesion and increased bleeding risk. Catamenial hemothorax, a rare manifestation of thoracic endometriosis, involves recurrent intrapleural bleeding in synchrony with menstruation. Coexistence of both conditions poses significant challenges to perioperative anesthetic management due to compounded risks of hemorrhage and respiratory complications. We report the successful anesthetic management of a 22-year-old woman with coexisting Bernard-Soulier syndrome and catamenial hemothorax who underwent thoracotomy and pleurodesis, along with a brief review of the relevant literature.
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Bernard-Soulier syndrome is a rare inherited bleeding disorder caused by a deficiency of the platelet surface glycoprotein Ib-IX-V complex, leading to defective platelet adhesion and increased bleeding risk. Catamenial hemothorax, a rare manifestation of thoracic endometriosis, involves recurrent intrapleural bleeding in synchrony with menstruation. Coexistence of both conditions poses significant challenges to perioperative anesthetic management due to compounded risks of hemorrhage and respiratory complications. We report the successful anesthetic management of a 22-year-old woman with coexisting Bernard-Soulier syndrome and catamenial hemothorax who underwent thoracotomy and pleurodesis, along with a brief review of the relevant literature. Case Report Readers Of this Article Also Read - Cervical Spine Fixation in a High-Risk Patient Using Continuous Thoracic Spinal ... - The Potential Impacts of Artificial Intelligence on Preoperative Optimization... - A Successful Use of Electromyography-Based Neuromuscular Monitoring in a... - Microaffirmations: The Way Forward - Preoperative Anesthesia Evaluation in a Patient With Hyperthyroidism and a...

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Condition tags

endometriosisthoracic_endometriosis

MeSH descriptors

Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome

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Source provenance

europepmc
last seen: 2026-08-08T06:08:32.324769+00:00
pubmed
last seen: 2026-08-08T06:04:55.559968+00:00
unpaywall
last seen: 2026-06-13T06:42:57.164913+00:00
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