Anesthetic Management of a Patient With Bernard-Soulier Syndrome and Catamenial Hemothorax for Thoracotomy: A Case Report

Suvarna Kaniyil, Ananya Soman, Indu Susheela
A&A practice · 2025 · vol. 19(10) , pp. e02064 · doi:10.1213/XAA.0000000000002064 · PMID:41117791
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Abstract

Bernard-Soulier syndrome is a rare inherited bleeding disorder caused by a deficiency of the platelet surface glycoprotein Ib-IX-V complex, leading to defective platelet adhesion and increased bleeding risk. Catamenial hemothorax, a rare manifestation of thoracic endometriosis, involves recurrent intrapleural bleeding in synchrony with menstruation. Coexistence of both conditions poses significant challenges to perioperative anesthetic management due to compounded risks of hemorrhage and respiratory complications. We report the successful anesthetic management of a 22-year-old woman with coexisting Bernard-Soulier syndrome and catamenial hemothorax who underwent thoracotomy and pleurodesis, along with a brief review of the relevant literature.
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Bernard-Soulier syndrome is a rare inherited bleeding disorder caused by a deficiency of the platelet surface glycoprotein Ib-IX-V complex, leading to defective platelet adhesion and increased bleeding risk. Catamenial hemothorax, a rare manifestation of thoracic endometriosis, involves recurrent intrapleural bleeding in synchrony with menstruation. Coexistence of both conditions poses significant challenges to perioperative anesthetic management due to compounded risks of hemorrhage and respiratory complications. We report the successful anesthetic management of a 22-year-old woman with coexisting Bernard-Soulier syndrome and catamenial hemothorax who underwent thoracotomy and pleurodesis, along with a brief review of the relevant literature. Case Report Readers Of this Article Also Read - Cervical Spine Fixation in a High-Risk Patient Using Continuous Thoracic Spinal ... - The Potential Impacts of Artificial Intelligence on Preoperative Optimization... - A Successful Use of Electromyography-Based Neuromuscular Monitoring in a... - Microaffirmations: The Way Forward - Preoperative Anesthesia Evaluation in a Patient With Hyperthyroidism and a...

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Condition tags

endometriosisthoracic_endometriosis

MeSH descriptors

Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome Bernard-Soulier Syndrome

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europepmc
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