Persistent Hypoxemia after PAPVC Correction :A Special Case Report

Partial anomalous pulmonary venous connection is a rare adult congenital heart disease that leads to an anatomical lefttoright shunt. Right superior pulmonary vein and azygos vein open to the superior vena cava, with atrial septal defect and severe pulmonary hypertension are also rare congenital anomalies that result in right-to-left shunt. A 52yearold male presented with dyspnea on exertion and fatigue. He was further diagnosed in our hospital and was found to have the aforementioned congenital abnormalities, causing a bidirectional shunt. On further investigation, he was found to have hypoxemia on oximetry. The patient was treated via surgical corrections of the congenital anomalies, but still showed persistent hypoxemia after the operation. After the related diseases were excluded through various examinations, we finally thought that hypoxemia was probably caused by pulmonary hypertension.