The World Allergy Organization journal

· 2 papers in corpus
2025
C1 esterase inhibitor (C1-INH) response as a supportive diagnostic criterion for patients with suspected hereditary angioedema with normal C1-INH.
doi:10.1016/j.waojou.2025.101125 ·PMID:41189715

Diagnosis of hereditary angioedema (HAE) with normal C1INH level (HAE-nl-C1INH) is based on several criteria, including either an associated genetic variant identified or family history of recurrent angioedema plus lack of high-dose antihis…

2022
Clinical profile and treatment outcomes in patients with hereditary angioedema with normal C1 esterase inhibitor.
doi:10.1016/j.waojou.2021.100621 ·PMID:35145604

BackgroundHereditary angioedema (HAE) is often caused by low serum levels or functional deficiency in C1 inhibitor (C1-INH); however, in some cases, C1-INH serum level and function are measured as normal (HAE-nl-C1INH). Management of HAE-nl…