{"paper_id":"ede97ad4-867b-4245-959f-ad639861d396","body_text":"Abstract\nClear cell carcinoma (CCC) of the female genital tract can arise in the ovary, endometrium, cervicovaginal region, in peritoneal and other extra pelvic sites. However, CCC involving anterior abdominal wall is a very rare entity. We are reporting a case of 55-year-old postmenopausal lady with ECOG PS-I with no comorbidity had history of cesarean section about 30 years back and presented with pain in abdomen at periumbilical region about 9 months back. She underwent evaluation at outside clinic with finding of an anterior abdominal wall swelling of size approximately 3 × 3 cm which was completely neglected by the patient. In the next period of 2 months, the swelling suddenly increased in size. CECT/PET CT showed a solid cystic mass involving anterior abdominal wall with possibility of desmoid tumor. We had decided to plan for surgical excision of the tumor. Intraoperatively we found that there was bicornuate uterus. The lesion was arising from one of the cornue of uterus and it was extended anteriorly to anterior abdominal wall with no ascites, no pelvic, or retroperitoneal lymphadenopathy. She underwent hysterectomy with bilateral salpingo-oophorectomy and defect was closed with bioabsorbable mesh. Final histopathology report was clear cell endometrial carcinoma mostly mullerian tract origin arising from endometriosis focus. Tumor cells were diffusely positive for PAX-8 and Napsin-A and negative for WT 1 with patchy positivity for P53 (wild type expression). She had received adjuvant chemotherapy and she is disease free after 2 years of completion of the treatment. 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Gynecol Oncol Rep 20:78–80\nAuthor information\nAuthors and Affiliations\nCorresponding author\nEthics declarations\nEthics Approval and Consent to Participate\nNot applicable.\nConflict of Interest\nThe authors declare no competing interests.\nHuman Subject\nInformed consent was obtained from the patient for being included in the study.\nFinancial Relationships\nAll authors have declared that they have no financial relationships at present or within the previous 3 years with any organizations that might have an interest in the submitted work.\nOther Relationships\nAll authors have declared that there are no other relationships or activities that could appear to have influenced the submitted work.\nConsent for Publication\nAn informed consent to publish this case was obtained from the patient.\nClinical Trial Transparency\nNot applicable\nGuarantor of submission\nThe corresponding author is the guarantor of submission.\nAdditional information\nPublisher’s Note\nSpringer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.\nRights and permissions\nAbout this article\nCite this article\nKadam, S.S., Deshmukh, S., Karandikar, S.M. et al. Does Preoperative Diagnosis Will Change the Treatment Plan of Clear Cell Carcinoma of Endometrium Masquerading as Desmoid Tumor of Anterior Abdominal Wall?: a Case Report. Indian J Surg Oncol 12 (Suppl 2), 312–318 (2021). https://doi.org/10.1007/s13193-021-01352-2\nReceived:\nAccepted:\nPublished:\nVersion of record:\nIssue date:\nDOI: https://doi.org/10.1007/s13193-021-01352-2","source_license":"CC0","license_restricted":false}