{"paper_id":"b1bbb73d-c06b-4cdb-934a-2a47af6e0345","body_text":"Abstract\nPurpose of Review\nDiscuss common and uncommon features of obstructed hemivagina with ipsilateral renal anomaly (OHVIRA), including diagnostic strategies, management, referral considerations, and the impact of OHVIRA on reproductive health throughout the patient’s lifespan. Coding and billing resources are also included to aid in accurately capturing the complexity of Müllerian anomalies.\nRecent Findings\nTwo-thirds of patients with OHVIRA have endometriosis on laparoscopy. Patients with OHVIRA experience normal fertility rates comparable to the general population, but may be at increased risk for certain pregnancy complications such as malpresentation and preterm delivery. Recent reports indicate there may be risk for rare forms of cervical cancer on the previously obstructed side. Strategies for recognition and management may differ in high resource versus low resource settings.\nSummary\nOHVIRA is a complex Müllerian anomaly, and diagnosis is often delayed. High resolution MRI is preferred for most accurate pre-surgical diagnosis, however this imaging modality may not be available in low resource settings. Development of accessible advanced imaging tools may provide improved diagnostic capabilities in limited resource settings. Medical management is appropriate for many patients until a comprehensive plan including post-operative considerations is finalized. Surgical correction should be performed by a specialist or subspecialist with appropriate training. 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All authors wrote the main manuscript text and reviewed the final manuscript.\nCorresponding author\nEthics declarations\nHuman and Animal Rights\nAll reported studies/experiments with human or animal subjects performed by the authors have been previously published and complied with all applicable ethical standards (including the Helsinki declaration and its amendments, institutional/national research committee standards, and international/national/institutional guidelines).\nCompeting interests\nThe authors declare no competing interests.\nConflict of interest\nThe authors have no conflicts of interest or disclosures.\nAdditional information\nPublisher’s Note\nSpringer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.\nRights and permissions\nSpringer Nature or its licensor (e.g. a society or other partner) holds exclusive rights to this article under a publishing agreement with the author(s) or other rightsholder(s); author self-archiving of the accepted manuscript version of this article is solely governed by the terms of such publishing agreement and applicable law.\nAbout this article\nCite this article\nMoon, L.M., O’Flynn O’Brien, K.L. & Dietrich, J.E. OHVIRA: An In-Depth Review with Practical Applications for OBGYNs Worldwide. Curr Obstet Gynecol Rep 14, 33 (2025). https://doi.org/10.1007/s13669-025-00441-1\nReceived:\nAccepted:\nPublished:\nVersion of record:\nDOI: https://doi.org/10.1007/s13669-025-00441-1","source_license":"CC0","license_restricted":false}