{"paper_id":"6d83c8c7-a290-4843-b2f6-35a121c3e13d","body_text":"Rare variant of unicornuate uterus with functional uterine horn and ipsilateral renal agenesis: a case report\nMain Article Content\nAbstract\nBackground: A unicornuate uterus is a rare congenital malformation of the Mullerian duct caused by incomplete development of one duct, often associated with obstructive complications and renal anomalies.\nCase presentation: A 12-year-old girl reported progressive left-sided lower abdominal pain and cyclical dysmenorrhea unresponsive to analgesics. Ultrasonography revealed hematometra, hematocolpos, and an absent left kidney. While MRI indicated a bicornuate uterus with hematometra, hematosalpinx, and a possible left endometriotic cyst, vaginoscopy showed a single right-sided cervix, ruling out hematocolpos. Diagnostic laparoscopy confirmed a right unicornuate uterus with a non-communicating functional left uterine horn, along with a left hematosalpinx and an endometriotic cyst. Surgical removal of the rudimentary horn, hematosalpinx, and endometriotic cyst was performed. The patient recovered well with relief of pain in subsequent menstrual cycles.\nConclusion: Early Ultrasound and MRI may facilitate the diagnosis, but laparoscopy provides definitive evaluation and management of such a rare congenital anomaly while preserving long-term reproductive health.\nArticle Details\nThis work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.\nReferences\nDixit R, Duggireddy CS, Pradhan GS. Mullerian anomalies: revisiting imaging and classification. Insights Imaging. 2025;16:40. doi:10.1186/s13244-024-01879-2\nObeidat RA, Aleshawi AJ, Tashtush NA, Alsarawi H. Unicornuate uterus with a rudimentary non-communicating cavitary horn in association with VACTERL association: case report. 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