{"paper_id":"2b61a42b-0a4d-42f0-878d-fa2bbf621477","body_text":"Abstract\nEntometrioid stromal sarcomas are seen in extra-uterine as well as extra-gonadal sites and have a strong association with endometriosis. Although having better prognosis than other sarcomas, yet these tumors may relapse (whether local or distant) in up to 56% of cases, even as late as 20 years after surgery. We report a case of a 30-year-old female patient with a mass in the inferior vena cava and right atrium which was surgically removed using cardiopulmonary bypass and deep hypothermic circulatory arrest and turned to be an entometrioid stromal sarcoma. The patient gave a history of endometriosis followed by the appearance of a low-grade ovarian endometrioid stromal sarcoma 4 years before the development of the mass in the IVC and right atrium.\nSimilar content being viewed by others\nReferences\nDiesing D, Cordes T, Finas D, Löning M, Mayer K, et al. Endometrial stromal sarcomas—a retrospective analysis of 11 patients. Anticancer Res. 2006;26:655–61.\nWong J, Tan G, Chia C, Selvarajan S, Teo M. A rare case of multiple malignancies arising in endometriosis: diffuse extra-uterine high-grade endometrial stromal sarcoma and ovarian carcinoma. Am J Cancer Case Rep. 2015;3:1–8.\nMourra N, Tiret E, Parc Y, de Saint-Maur P, Parc R, et al. Endometrial stromal sarcoma of the rectosigmoid colon arising in extragonadal endometriosis and revealed by portal vein thrombosis. Arch Pathol Lab Med. 2001;125:1088–90.\nAlaaraj R, Lataifeh I, Elsaadi J, Salameh M, Sughayer M. Primary low-grade endometrioid stromal sarcoma of the ovary with multiple omental metastases. Gulf Med J. 2016;5:69–73.\nAli RH, Rouzbahman M. Endometrial stromal tumors revisited: an update based on the 2014 WHO classification. J Clin Pathol. 2015;68:325–32.\nAl-Ebrahim KE. Right atrial mass: the dilemma of diagnosis and when not to operate (letter). Ann Thorac Surg. 2009;87:2005.\nLauten A, Strauch JT, Wippermann J, Wahlers T. A rare type of right atrial tumor in a 66-year-old woman. J Thorac Cardiovasc Surg. 2007;133:251–2.\nChiappini B, Savini C, Marinelli G, Martin Suarez S, DiEusanio M, et al. Cavoatrial tumor thrombus: single-stage surgical approach with profound hypothermia and circulatory arrest, including a review of the literature. J Thorac Cardiovasc Surg. 2002;124:684–8.\nAuthor information\nAuthors and Affiliations\nCorresponding author\nEthics declarations\nConflict of interest\nThe authors have no conflict of interest to declare.\nRights and permissions\nAbout this article\nCite this article\nAlkady, H., Abouramadan, S., Nagy, M. et al. Removal of an endometrioid stromal sarcoma from the inferior vena cava and right atrium. Gen Thorac Cardiovasc Surg 67, 324–327 (2019). https://doi.org/10.1007/s11748-018-0902-5\nReceived:\nAccepted:\nPublished:\nVersion of record:\nIssue date:\nDOI: https://doi.org/10.1007/s11748-018-0902-5","source_license":"CC0","license_restricted":false}